Search on: CYSTEINE DESULFHYDRASE 
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Descriptor English:   Cystathionine gamma-Lyase 
Descriptor Spanish:   Cistationina gamma-Liasa 
Descriptor Portuguese:   Cistationina gama-Liase 
Synonyms English:   Cystine Desulfohydrolase
Cystathionine gamma Lyase
Deaminase, Homoserine
Dehydratase, Homoserine
Desulfhydrase, Cysteine
Desulfhydrase, Cystine
Desulfohydrolase, Cystine
gamma Cystathionase
gamma-Lyase, Cystathionine
Cystathionase
Cysteine Desulfhydrase
Cystine Desulfhydrase
gamma-Cystathionase
Homoserine Deaminase
Homoserine Dehydratase  
Tree Number:   D08.811.520.300.250
Definition English:   A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1. 
Indexing Annotation English:   /defic: consider also CYSTATHIONINE /urine (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM)
History Note English:   91(75); was see under LYASES 1975-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   3561 
Unique Identifier:   D003542 

Occurrence in VHL:
 

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